Supplementary Table 1

Main functions: surfactant delivery and epithelial repair

Function/product
Functional significance
Reference

Surfactant


     Synthesis


     Components of surfactant


          Phospholipids
Surface activity
[186]
          Surfactant proteins


               A
Tubular myelin formation
[71,187,188]

Defence
[33]
               B
Absorption of lipid to monolayer
[71,189]
               C

[86]
               D
Defence
[34,190]
     Components secreted together with surfactant


          Lysozyme
Defence
[35,191]
          Plasmalogens
Protection against oxidation
[192]
          Cathepsin H


     Maturation


          Intracellular cathepsin H
Processing of SP-B
[194]

Processing of SP-C
[50]
     Secretion


     Signal receptors


          β-adrenergic receptors

[195,196]
          P1 purinoreceptors

[197,198]
          P2Y purinoreceptors

[198,199]
     Components of exocytosis apparatus


          Microtubules

[65]
          Actin

[66]
          Annexin II

[200]
          Annexin IV

[201]
          Annexin VII (= Synexin)

[202,203]
     Extracellular transformation


          α1-antitrypsin

[2048]
          Convertase
Conversion of lipid monolayer into vesicles
[88,89,205]
     Recycling


          Receptor of SP-A

[206]
          Lamellar body lysosomal enzymes


               Alkaline phosphatase
Marker of type II cells
[207]
               α-glucosidase

[208]
               α-mannose

[208]
Alveolar epithelial repair


     Proliferation


          Cyclin A

[209]
          Cyclins D1, D2
Proliferation, differentiation
[210]
          Cyclin dependent phosphokinases
Proliferation, differentiation
[210]
          PTHRP
Inhibition of proliferation
[211]
          Calmodulin
Proliferation, differentiation
[212,213]
          Insulin-like growth factor (IGF)-binding protein2
G1-arrest
[214]
     Differentiation


          Retinoic acid receptor
Inhibition of differentiation
[215]
          Aminopeptidase N

[216]
     Apoptosis


          CD95 (receptor of Fas-ligand)

[134]
          Fas-ligand

[138]
          Bax
Pro-apoptotic peptide
[217]
          Bcl-2
Anti-apoptotic peptide
[138]
          Caspase-3
Execution caspase
[138]

Fehrenbach Respiratory Research 2001 2:33   doi:10.1186/rr36